Mimicker of hereditary angioedema: Idiopathic systemic capillary leak syndrome successfully treated with intravenous immunoglobulin

Idiopathic systemic capillary leak syndrome (ISCLS) is a rare, potentially life-threatening disease characterized by episodic attacks of systemic capillary hyperpermeability and vascular collapse accompanied by hypoalbuminemia, hemoconcentration, and edema.1–3 We describe the case of a 46-year-old man with recurrent abdominal pain and facial edema, long believed to have recurrent angioedema, who was ultimately diagnosed with ISCLS.

http://ift.tt/2ouX53E