Anterior Skull Base Duplication Requiring Delivery Via EXIT Procedure: A Case Report

Publication date: Available online 14 September 2018

Source: International Journal of Pediatric Otorhinolaryngology

Author(s): Courtney B. Shires, Jonathan P. Giurintano, Jennifer McLevy-Bazzanella, Jerome Thompson

Abstract

Duplication of the anterior skull base structures is an extremely rare malformation of failed midline blastogenesis. We present the case of a child with an obstructive oral cavity mass diagnosed on prenatal imaging. The child was successfully delivered by EXIT procedure, a tracheotomy was performed, and postnatal imaging demonstrated an array of craniofacial malformations, including complete duplication of the maxilla, pituitary glands, aqueducts of Sylvius, and basilar arteries. The child underwent excision of the duplicate maxilla, resulting in a wide cleft palate that will be repaired at a future date.

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