IgA tracheobronchial deposits underlie respiratory compromise in neonatal linear IgA bullous dermatosis

Abstract

The childhood variant of linear IgA bullous dermatosis (LABD) is characterized by blistering lesions of the perineum and perioral area with an annular or "rosette-like" arrangement, in addition to the pathognomonic linear IgA deposits along the cutaneous basement membrane zone (BMZ).¹ The disease mainly occurs in preschool children.¹ However, a handful of neonatal cases have been described, most of them presenting with severe mucosal involvement.^2-8 We report an additional case of neonatal LABD with life-threatening respiratory tract manifestations.

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