Unusual case of hemiarhinia

Description

A boy aged 9 years presented to our clinic with the absence of the left side of the nose (figures 1 and 2). There was no symptom of difficulty in nasal breathing and parents were only concerned regarding facial disfigurement. The boy was born at full term via a normal vaginal delivery and the antenatal period was uneventful. There was neither any history of consanguinity nor similar symptoms in the family. On examination, the lower two-third of the left side of the nose was absent with marked deviation of the nasal septum towards the right. There was gaze nystagmus with left esotropia on ophthalmological examination. High-resolution CT showed bilaterally symmetrical nasal bones with rudimentary right nasal cavity. There was marked deviation of the nasal septum towards the right with hypoplastic left-sided paranasal sinuses (figure 3). Extensive screening for congenital malformations in...

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