A rare sporadic case of Camurati Engelmann disease with jaw involvement

Publication date: Available online 14 April 2017
Source:Journal of Oral and Maxillofacial Surgery
Author(s): Maria Fyrgiola, Violeta Lianou, Konstantinos Katoumas, Ioannis Dimopoulos
Camurati-Engelmann disease (CED), or progressive diaphyseal dysplasia, is an uncommon bone dysplasia, which is inherited in an autosomal dominant pattern. The disease mainly affects the diaphyses of the long bones, but can also induce sclerotic changes to the facial skeleton and the skull base. The diagnosis of CED is based on clinical and radiological features. The purpose of the article is to present the clinical and radiological characteristics of the jaws, as shown in cone-beam computed tomography images of a 46-year old-female diagnosed with CED.



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